Dentinogenesis imperfecta type II: a case report

Authors

  • Bruno Carvalho Albeny Morais Centro Universitário Católica do Leste de Minas Gerais
  • Daniel Alves Leite Centro Universitário Católica do Leste de Minas Gerais
  • Frederico Marques da Silva Centro Universitário Católica do Leste de Minas Gerais
  • Gabriela Caldeira Andrade Americano Centro Universitário Católica do Leste de Minas Gerais
  • Erika Storck Cezário Centro Universitário Católica do Leste de Minas Gerais

DOI:

https://doi.org/10.11606/issn.2357-8041.clrd.2021.172836

Keywords:

Dentinogenesis imperfecta, Diagnosis, Case report

Abstract

Objective: Dentinogenesis imperfecta (DI) type II is a rare dentin development disorder with an autosomal dominant inheritance that affects both functional and aesthetic aspects of deciduous and permanent dentitions. This study reports the clinical case of a patient diagnosed late with this anomaly. Material and methods: Male patient, 33 years old, sought dental care complaining of dental aesthetic dissatisfaction. During clinical examination, it was observed that the teeth had a brownish color, with wear and tear of the dental enamel and dentin exposure. Radiographically, the teeth presented the pulp chambers and root canals obliterated, in addition to bulbous crowns. The patient reported that several members of his family had the same condition. The established clinical diagnosis was DI type II. Conclusion: In this case, type II dentinogenesis imperfecta was diagnosed late and without adequate therapeutic intervention, causing aesthetic and functional damage to the patient.

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Author Biographies

  • Bruno Carvalho Albeny Morais, Centro Universitário Católica do Leste de Minas Gerais

    Dental Medicine School, Centro Universitário Católica do Leste de Minas Gerais (Unileste), Ipatinga, MG, Brazil

  • Daniel Alves Leite, Centro Universitário Católica do Leste de Minas Gerais

    Dental Medicine School, Centro Universitário Católica do Leste de Minas Gerais (Unileste), Ipatinga, MG, Brazil

  • Frederico Marques da Silva, Centro Universitário Católica do Leste de Minas Gerais

    Dental Medicine School, Centro Universitário Católica do Leste de Minas Gerais (Unileste), Ipatinga, MG, Brazil

  • Gabriela Caldeira Andrade Americano, Centro Universitário Católica do Leste de Minas Gerais

    Dental Medicine School, Centro Universitário Católica do Leste de Minas Gerais (Unileste), Ipatinga, MG, Brazil

  • Erika Storck Cezário, Centro Universitário Católica do Leste de Minas Gerais

    Dental Medicine School, Centro Universitário Católica do Leste de Minas Gerais (Unileste), Ipatinga, MG, Brazil

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Published

2021-02-25

Issue

Section

Case report or technical report

How to Cite

Morais, B. C. A., Leite, D. A., Silva, F. M. da, Americano, G. C. A., & Cezário, E. S. (2021). Dentinogenesis imperfecta type II: a case report. Clinical and Laboratorial Research in Dentistry. https://doi.org/10.11606/issn.2357-8041.clrd.2021.172836