Aspectos bucais da síndrome de Rubinstein-Taybi: relato de dois casos clínicos

Authors

DOI:

https://doi.org/10.11606/issn.2357-8041.clrd.2017.139579

Keywords:

Rubinstein-Taybi Syndrome, Oral Manifestations, Case Report

Abstract

Rubinstein-Taybi syndrome is a rare genetic multisystem disorder characterized by typical facial dimorphism, slow growth, mental deficiency, and multiple dental abnormalities. This case report describes the oral-facial findings of Rubinstein-Taybi syndrome affecting a 11-year-old Brazilian male, and a 10-year-old female. The oral findings of the patients, such as thin upper lips, prolonged retention of the primary teeth, and hypodontia are reported, and the clinical management is discussed.

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Author Biographies

  • Fabiana Mesquita Barros, University of São Paulo

    Departamento de Estomatologia, Faculdade de Odontologia, Universidade de São Paulo, São Paulo, SP, Brasil

  • Letycia Iida, University of São Paulo

    Graduanda, Faculdade de Odontologia, Universidade de São Paulo, São Paulo, SP, Brasil

  • Aparecida Angélica Castorino, University of São Paulo

    Departamento de Estomatologia, Faculdade de Odontologia, Universidade de São Paulo, São Paulo, SP, Brasil

  • Fabiana Martins, University of São Paulo

    Departamento de Estomatologia, Faculdade de Odontologia, Universidade de São Paulo, São Paulo, SP, Brasil

  • Marina Gallotini, University of São Paulo

    Departamento de Estomatologia, Faculdade de Odontologia, Universidade de São Paulo, São Paulo, SP, Brasil

References

Published

2018-03-13

Issue

Section

Case report or technical report

How to Cite

Barros, F. M., Iida, L., Alves, T. D., Castorino, A. A., Martins, F., & Gallotini, M. (2018). Aspectos bucais da síndrome de Rubinstein-Taybi: relato de dois casos clínicos. Clinical and Laboratorial Research in Dentistry. https://doi.org/10.11606/issn.2357-8041.clrd.2017.139579