Telangiectasia hereditária familiar: uma causa rara de trombose de porta
DOI:
https://doi.org/10.11606/issn.1679-9836.v103i5e-227301Palavras-chave:
Trombose de Porta, Epixtase, Telangiectasia Hemorrágica HereditáriaResumo
Telangiectasia hemorrágica hereditária (THH) é uma doença autossômica dominante que cursa com malformações arteriovenosas que afetam pele, pulmões, cérebro, superfícies mucosas e trato gastrointestinal. A doença se apresenta de diversas formas clínicas como epistaxe, sangramento gastrointestinal e sintomas decorrentes das malformações arteriovenosas cerebrais e pulmonares. A THH confere risco aumentado para tromboembolismo venoso. Apresentamos uma mulher de 57 anos com THH que apresentou epistaxe de repetição, shunt arteriovenoso pulmonar e trombose de porta com transformação cavernomatosa. Ela foi submetida a cauterização nasal, embolização pulmonar, e anticoagulação. A paciente recebeu alta hospitalar com remissão dos sintomas e rivaroxabana oral.
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Copyright (c) 2024 Antônio Erisvaldo Linhares Ponte Filho, Dr. Aglaêrton Silva Pinheiro, Rafael Siqueira Athayde Lima
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