Frantz’s tumor in a female patient with diarrhea: case report of a rare pancreatic neoplasm

Authors

  • Luis Arthur Brasil Gadelha Farias Faculdade de Medicina, Universidade Federal do Ceará (UFC), Fortaleza, Ceará, Brasil
  • Danielle Souza Carvalho Maciel Faculdade de Medicina, Universidade Estadual do Ceará (UECE), Fortaleza, Ceará, Brasil
  • Mariana Silton Pinheiro de Araujo Faculdade de Medicina, Centro Universitário Christus (UNICHRISTUS), Fortaleza, Ceará, Brasil.
  • Angélica Maria Holanda Pascoal da Silva Serviço de Gastroenterologia, Hospital Geral de Fortaleza (HGF), Fortaleza, Ceará, Brasil
  • Rebeca Viana Brígido de Moura Cairutas Serviço de Gastroenterologia, Hospital Geral de Fortaleza (HGF), Fortaleza, Ceará, Brasil
  • Débora Praciano Correia Férrer Leite Serviço de Gastroenterologia, Hospital Geral de Fortaleza (HGF), Fortaleza, Ceará, Brasil
  • Gardênia Costa do Carmo Serviço de Gastroenterologia, Hospital Geral de Fortaleza (HGF), Fortaleza, Ceará, Brasil
  • Francisco Sérgio Rangel de Paula Pessoa Serviço de Gastroenterologia, Hospital Geral de Fortaleza (HGF), Fortaleza, Ceará, Brasil

DOI:

https://doi.org/10.11606/issn.1679-9836.v97i2p248-251

Keywords:

Pancreatic neoplasms/therapy, Abdominal pain, Diarrhea, Weight loss.

Abstract

Solid pseudopapillary tumor, also known as frantz tumor, is a rare tumor of the pancreas. We report a case of 25-year-old female patient with abdominal pain, fever, diarrhea and weight loss. Contrast abdominal CT showed enlarged pancreas with a hypodense lesion of nodular appearance and peripheral calcifications.It was decided to perform subtotal pancreatectomy with lymphadenectomy, and opted for splenectomy and intraoperative liver biopsy. The pathology of surgical resection of the pancreatic tumor showed solid pseudopapillary tumor compatible with Frantz’s tumor. Immunohistochemistry confirmed histopathological findings. She evolved with pancreatic fistula and pancreatitis resolved after 15 days. Currently, it is being followed up in our service with complete remission of symptoms.

Downloads

Download data is not yet available.

References

Downloads

Published

2018-06-15

Issue

Section

Relato de Caso/Case Report

How to Cite

Farias, L. A. B. G., Maciel, D. S. C., de Araujo, M. S. P., da Silva, A. M. H. P., Cairutas, R. V. B. de M., Leite, D. P. C. F., Carmo, G. C. do, & Pessoa, F. S. R. de P. (2018). Frantz’s tumor in a female patient with diarrhea: case report of a rare pancreatic neoplasm. Revista De Medicina, 97(2), 248-251. https://doi.org/10.11606/issn.1679-9836.v97i2p248-251