Adult urticaria pigmentosa: successful treatment in association with phototherapy
DOI:
https://doi.org/10.11606/issn.1679-9836.v99i4p400-404Keywords:
Urticária pigmentosa, Mastocytosis, cutaneous, Mastocytosis, systemicAbstract
Introduction: Adult urticaria pigmentosa is a rare and persistent form of mastocytosis, often with systemic manifestations and involvement of the bone marrow, and less evident cutaneous manifestations, contrary to what occurs in childhood. Objective: The authors aim to report a case of adult onset, with mild skin lesions, and development of symptoms of histamine release, without systemic involvement. Methodology: The information was obtained through review of the medical record, interview with the patient, photographic record, and a literature review. Conclusion: The correct diagnosis and the early assessment of involvement of other organs is important, as well as adequate treatment and prevention of anaphylactoid reactions. Phototherapy is an interesting treatment option for refractory cases.
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References
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