Erdheim-Chester disease: case report

Authors

DOI:

https://doi.org/10.11606/issn.1679-9836.v100i3p303-305

Keywords:

Immunohistochemistry, Xanthogranuloma, Erdheim-Chester disease

Abstract

Erdheim-Chester disease is a rare non-Langerhans cell histiocytosis, first described by Jakob Erdheim and William Chester in 1930 of unknown etiology. Clinically, it can reach all organs and systems and the diagnosis is based on radiological and anatomopathological findings. It was reported a case of the disease where the clinical, radiological and anatomopathological findings.

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Author Biographies

  • Aline Alencar Giongo, Rede D’Or

    Rede D’Or, Anatomia Patológica. 

  • Bruno Santos Leal Campos, Hospital HOME

    Hospital HOME, Ortopedia. 

  • Tercia Jovino Neves Santos, Diagnósticos da América (DASA)

    Diagnósticos da América (DASA), Anatomia Patológica. 

  • Felipe D'Almeida Costa, AC Camargo Cancer Center

    A. C. Camargo Cancer Center, Anatomia Patológica.

References

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Published

2021-07-30

Issue

Section

Relato de Caso/Case Report

How to Cite

Giongo, A. A. ., Campos, B. S. L. ., Santos, T. J. N., & Costa, F. D. (2021). Erdheim-Chester disease: case report. Revista De Medicina, 100(3), 303-305. https://doi.org/10.11606/issn.1679-9836.v100i3p303-305