Association of Hirschsprung’s disease and Ladd’s band in a newborn
DOI:
https://doi.org/10.11606/issn.1679-9836.v101i5e-165550Keywords:
Hirschsprung disease, Congenital abnormalities, Constipation, Intestinal obstructionAbstract
Introduction: Hirschsprung’s disease, also known as congenital megacolon, presents alterations in the distal enteric innervation. During the neonatal period, it presents through the classical triad of vomiting, abdominal distension and delayed meconium elimination. Objective: To describe clinical case of a male patient diagnosed with congenital megacolon, whose initial presentation was neonatal intestinal obstruction attributed to congenital adhesion bands and intestinal malrotation and Hirschsprung’s disease. Comments: Although it is a congenital disease, the diagnosis does not always occur during the neonatal period and should be considered in the diagnostic reasoning of older patients with a history of constipation refractory to treatment. Approximately 20% of children have negative outcomes on the postoperative course, with constipation being the most common complaint, tending to improve over the years. No association was found in the literature with congenital band, intestinal malrotation and Hirschsprung’s disease.
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