Fahr´s syndrome after thyroidectomy: a case report

Authors

DOI:

https://doi.org/10.11606/issn.1679-9836.v100i5p503-507

Keywords:

Fahr's syndrome, Calcification, Basal nucleus, Hypoparathyreoidism

Abstract

Fahr´s syndrome is a rare disease characterized by bilateral symmetrical calcification over the basal ganglion of the brain and nuclei dentate of cerebellum mainly resulting from disorders in calcium-phosphorus metabolism. Neuropsychiatric changes and extrapyramidal symptoms are one of the main clinical manifestations described. Computed tomography is the imaging method used for visualizing brain calcifications and when associated with clinical history and laboratory findings is a triad for definitive diagnosis. Therefore, the objective of this was to report the clinical case of a patient with Fahr Syndrome presenting cranium brain computed tomography with symmetrical calcifications associated with a cognitive deterioration and extrapyramidal signs resulting from changes in calcium metabolism, having hypoparathyroidism as an etiological cause.

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Author Biographies

  • Aline do Socorro Lima Kzam, Centro Universitário Metropolitano da Amazônia - UNIFAMAZ

    Médica. Graduada pelo Centro Universitário Metropolitano da Amazônia - UNIFAMAZ, Belém (PA), Brasil. 

  • Adenard Francisco Cleophas Cunha, Centro Universitário Metropolitano da Amazônia - UNIFAMAZ

    Médico intensivista. Doutorando. Professor de Habilidades Clínicas do Centro Universitário Metropolitano da Amazônia-UNIFAMAZ, Belém (PA), Brasil.

  • Rebeca da Paixão Cleophas Cunha, Universidade do Estado do Pará - UEPA

    Médica. Graduada pela Universidade do Estado do Pará – UEPA, Belém (PA), Brasil

  • Marcel Atilia Silva Aguiar, Centro Universitário do Pará - CESUPA

    Graduando em Medicina no Centro Universitário do Pará – CESUPA, Belém (PA), Brasil.

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Published

2021-12-10

Issue

Section

Relato de Caso/Case Report

How to Cite

Kzam, A. do S. L., Cunha, A. F. C., Cunha, R. da P. C., & Aguiar, M. A. S. (2021). Fahr´s syndrome after thyroidectomy: a case report. Revista De Medicina, 100(5), 503-507. https://doi.org/10.11606/issn.1679-9836.v100i5p503-507