Retinal alterations in patients with sickle cell disease: a case series
uma série de casos
DOI:
https://doi.org/10.11606/issn.1679-9836.v100i2p193-196Keywords:
Retina, Ophtalmology, Fundus oculi, Anemia, sickle cellAbstract
This study aims to evaluate the main fundoscopic findings in patients with sickle cell hemoglobinopathy, observing which are the most common retinal alterations in this group. A retrospective and descriptive study was carried out using fundoscopies and retinographies of 34 patients accompanied by a specialized ophthalmology service and by the State of Alagoas. The most commonly found type of hemoglobinopathy was SS, followed by SC and S-thal hemoglobinopathies. Of the total of patients evaluated, 58.8% were male. 29.41% of the patients presented retinal alterations. As for genotype, 42.86% of the patients with genotype SC had retinal changes.A small number of retinal changes were observed in the studied sample, and all patients with signs of sickle cell retinopathy presented hemoglobinopathy of type SS or SC. The SS genotype was the most prevalent of the patients, but the SC genotype was the most at risk for developing retinal alterations.
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Copyright (c) 2021 João Vitor de Omena Jucá , Anna Luyza Correia dos Santos Alves, Carlos Eduardo Ximenes da Cunha, Caio Victor Oliveira Ferreira, Isaac Carvalho de Oliveira Ramos, Marina Viegas Moura Rezende Ribeiro
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