Behçet's disease: a diagnosis to remember

Authors

DOI:

https://doi.org/10.11606/issn.2176-7262.rmrp.2025.221744

Keywords:

Case report, Behçet's syndrome, Oral ulcers, Erythema nodosum, Therapeutics

Abstract

Behçet's disease is a rare condition characterized by systemic vasculitis of unknown etiology. In Brazil, it predominantly affects women with milder symptoms and better prognosis, and the diagnosis is clinical and supported by international criteria. The main differential diagnoses include sexually transmitted infections (STIs) such as syphilis, genital herpes and HIV/ AIDS. We report the case of a patient with a typical clinical picture (genital ulcers, oral ulcers and erythema nodosum) associated with compatible histopathological findings and immunohistochemical panel (positivity for CD20, CD3, CD68 and Ki-67). Combined treatment with systemic corticosteroids and colchicine was instituted, with complete resolution.

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Author Biographies

  • Natália Marcondes Garzon Lama, Universidade de Taubaté, Taubaté, (SP), Brasil

    Graduanda de Medicina 

  • Rafaela Fortes Viégas, Universidade de Taubaté, Taubaté, (SP), Brasil

    Graduanda de Medicina

  • Raquel de Almeida Prado Rocchi Domeneghetti, Universidade de Taubaté, Taubaté, (SP), Brasil

    Graduanda de Medicina 

  • Fábio Augusto Peroni Garcia, Hospital Municipal Universitário de Taubaté, Taubaté, (SP), Brasil

    Médico

  • Flavia Regina Ferreira, Universidade de Taubaté, Taubaté, (SP), Brasil

    Doutora

References

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Scherrer MAR, Castro LPF, Rocha VB, et al. Dermatoscopia no teste cutâneo da patergia: série de casos de pacientes com suspeita de Doença de Behçet. Revista Brasileira de Reumatologia. 2014; 54(6):494-98.

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Published

2025-12-16

Issue

Section

Relato de Caso

How to Cite

1.
Lama NMG, Viégas RF, Domeneghetti R de APR, Garcia FAP, Ferreira FR. Behçet’s disease: a diagnosis to remember. Medicina (Ribeirão Preto) [Internet]. 2025 Dec. 16 [cited 2026 Feb. 1];58(2):e-221744. Available from: https://revistas.usp.br/rmrp/article/view/221744