Agenesis of right pulmonary artery
case report
DOI:
https://doi.org/10.11606/issn.2176-7262.v53i1p61-65Keywords:
Agenesis, Pulmonary Artery, PathologyAbstract
Pulmonary artery agenesis is a rare congenital malformation, which occurs due to the non-development of the sixth aortic arch. However, it is not related to cardiac malformation, and also the intrapulmonary arteries, as well as the pulmonary vascularization and the bronchial tree usually do not change. In the present case study, the patient presents fever, productive cough, and tachypnea. A simple chest X-ray was performed because of the clinic, demonstrating right perihilar interstitial-alveolar opacity with right mediastinal deviation and asymmetry of pulmonary transparency. Due to the radiological finding, a computed tomography of the chest was requested, which showed the right lung of reduced volume. To provide a better understanding of the condition, the radiology team suggested computed angiotomography of the chest, which detected agenesis of the right pulmonary artery. The importance of the problem is to report a case of agenesis of the right pulmonary artery.
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Copyright (c) 2020 Ingred Stephany Domingues da Silva, Eugênio Fernandes de Magalhães, Letícia Carolina Malaquias Pereira, Luiza de Castro Cançado Braga, Victor Zenatti Femía, Cairo Barcelos Alves Serrano, Ana Luíza Rezende Collani, Paula Vieira Penha
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