Intraoperative diagnosis of retroperitoneal paraganglioma in abdominal mass
case report
DOI:
https://doi.org/10.11606/issn.2176-7262.v52i4p343-347Keywords:
Paraganglioma, Retroperitoneal Paraganglioma, Pheochromocytoma, Differential DiagnosisAbstract
Study design: case report; Relevance of the Problem: we herein report the case of a 40-year-old male patient, presented with pain in the left lumbar region for six months, with no palpable masses in the region and no retroperitoneal masses detected upon abdominal ultrasonography. The diagnostic investigation revealed, through Computed Tomography scans of the abdomen, an image of retroperitoneal lesion attached medially to the aorta artery, with the presumed diagnosis of Retroperitoneal Sarcoma and, consequently, indication for surgical treatment. During the intraoperative period, the patient presented adrenergic symptoms, which ceased after complete resection of the lesion and ligation of part of the tumor adhesions to the retroperitoneum. The biopsy revealed a Retroperitoneal Paraganglioma. The aforementioned case study illustrates the importance of including Paraganglioma as a differential diagnosis of retroperitoneal tumors, given its rarity, difficult diagnosis, and clinical importance. Comments: Paragangliomas, often called extra-adrenal pheochromocytomas, are rare, mostly benign, catecholamine-producing tumors originating from Autonomic Nervous System and neural crest cells1. The classic symptoms of these tumors, due to secretory capacity, include palpitations, headaches, and diaphoresis, associated with Arterial Hypertension (AHT).
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